Time to think beyond sickle cell screening and haemoglobin electrophoresis: a case report and review of literature of sickle cell D-Punjab falsely labelled as sickle cell SS from central India

نویسندگان

چکیده

Sickle cell haemoglobin D disease (D-Punjab) is a rare variant of sickle (SCD) reported from central India. Exact incidence pulmonary thrombosis in patients with HbSD unknown. Pulmonary known complication SCD but case pattern. We 34-year-old male patient acute chest syndrome (ACS). CT angiogram revealed near complete right middle lobe segmental and subsegmental branches infarct. Our responded to anticoagulant therapy. This report reminder that HPLC should be done all along solubility test hemoglobin electrophoresis detect exact

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ژورنال

عنوان ژورنال: International Journal of Research in Medical Sciences

سال: 2022

ISSN: ['2320-6012', '2320-6071']

DOI: https://doi.org/10.18203/2320-6012.ijrms20223104